{"id":25674,"date":"2019-09-12T15:44:47","date_gmt":"2019-09-12T13:44:47","guid":{"rendered":"https:\/\/hellocare.com\/?p=25674"},"modified":"2025-12-05T10:13:03","modified_gmt":"2025-12-05T09:13:03","slug":"maladie-de-charcot-symptomes-causes-et-traitement","status":"publish","type":"post","link":"https:\/\/www.hellocare.com\/blog\/maladie-de-charcot-symptomes-causes-et-traitement\/","title":{"rendered":"Maladie de Charcot : sympt\u00f4mes, causes et traitement"},"content":{"rendered":"<p><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-1 nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-0 fusion_builder_column_1_1 1_1 fusion-one-full fusion-column-first fusion-column-last\" style=\"--awb-bg-size:cover;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-column-wrapper-legacy\"><div class=\"fusion-text fusion-text-1\"><p><span style=\"font-size: regular;\"><span style=\"font-size: 18px; line-height: 1.6em; letter-spacing: 0px;\"><span class=\"fusion-dropcap dropcap\">L<\/span>a maladie de Charcot \u2013 aussi appel\u00e9e <strong>scl\u00e9rose lat\u00e9rale amyotrophique<\/strong>, <strong>SLA ou maladie de Lou Gehrig<\/strong> \u2013 est une maladie qui touche le syst\u00e8me nerveux. Mise en lumi\u00e8re par le c\u00e9l\u00e8bre astrophysicien Stephen Hawking qui en \u00e9tait atteint, elle reste pourtant assez m\u00e9connue. Mais quelles sont les <strong>causes de la maladie de Charcot<\/strong> ? Quels en sont les sympt\u00f4mes ? Comment <strong>diagnostiquer une SLA<\/strong> ?<\/span><\/span><\/p>\n<p><span style=\"font-size: regular;\"><!--more--><\/span><\/p>\n<\/div><div class=\"fusion-clearfix\"><\/div><\/div><\/div><\/div><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-2 nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-1 fusion_builder_column_1_1 1_1 fusion-one-full fusion-column-first fusion-column-last\" style=\"--awb-bg-size:cover;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-column-wrapper-legacy\"><div class=\"fusion-image-element in-legacy-container\" style=\"--awb-caption-title-font-family:var(--h2_typography-font-family);--awb-caption-title-font-weight:var(--h2_typography-font-weight);--awb-caption-title-font-style:var(--h2_typography-font-style);--awb-caption-title-size:var(--h2_typography-font-size);--awb-caption-title-transform:var(--h2_typography-text-transform);--awb-caption-title-line-height:var(--h2_typography-line-height);--awb-caption-title-letter-spacing:var(--h2_typography-letter-spacing);\"><span class=\" fusion-imageframe imageframe-none imageframe-1 hover-type-none\"><img decoding=\"async\" width=\"768\" height=\"513\" alt=\"musicotherapie\" title=\"Maladie de Charcot\" src=\"data:image\/svg+xml,%3Csvg%20xmlns%3D%27http%3A%2F%2Fwww.w3.org%2F2000%2Fsvg%27%20width%3D%27768%27%20height%3D%27513%27%20viewBox%3D%270%200%20768%20513%27%3E%3Crect%20width%3D%27768%27%20height%3D%27513%27%20fill-opacity%3D%220%22%2F%3E%3C%2Fsvg%3E\" data-orig-src=\"https:\/\/www.hellocare.com\/wp-content\/uploads\/2019\/09\/maladie-de-charcot.jpg\" class=\"lazyload img-responsive wp-image-25684\"\/><\/span><\/div><div class=\"fusion-clearfix\"><\/div><\/div><\/div><\/div><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-3 nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-2 fusion_builder_column_1_1 1_1 fusion-one-full fusion-column-first fusion-column-last\" style=\"--awb-bg-size:cover;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-column-wrapper-legacy\"><div class=\"fusion-title title fusion-title-1 fusion-sep-none fusion-title-text fusion-title-size-three\"><h3 class=\"fusion-title-heading title-heading-left fusion-responsive-typography-calculated\" style=\"margin:0;--fontSize:40;line-height:1.3;\"><h3>La maladie de Charcot c\u2019est quoi ?<\/h3><\/h3><\/div><div class=\"fusion-text fusion-text-2\"><p>Tout d\u2019abord, il faut dire que <strong>la maladie de Charcot est une maladie neurod\u00e9g\u00e9n\u00e9rative<\/strong>, c\u2019est-\u00e0-dire qu\u2019elle attaque les neurones, et plus particuli\u00e8rement les neurones responsables du contr\u00f4le des muscles. Elle se manifeste par une d\u00e9g\u00e9n\u00e9rescence rapide des fonctions motrices du corps comme par exemple le contr\u00f4le des membres ou de la d\u00e9glutition.<\/p>\n<p><strong>Qui peut \u00eatre atteint ?<\/strong><\/p>\n<p>C\u2019est une maladie qui touche en majorit\u00e9 des <strong>personnes \u00e2g\u00e9es de 40 \u00e0 60 ans<\/strong>, mais la SLA peut aussi apparaitre chez des patients plus jeunes ou plus \u00e2g\u00e9s. De m\u00eame, la maladie de Charcot touche aussi bien <strong>les hommes que les femmes<\/strong>, globalement \u00e0 \u00e9galit\u00e9 (avec une tr\u00e8s l\u00e9g\u00e8re majorit\u00e9 d\u2019hommes). Enfin, si toutes les ethnies sont concern\u00e9es, les blancs caucasiens sont plus touch\u00e9s que les populations noires, hispaniques ou asiatiques.<\/p>\n<p><strong>Quelle est l\u2019esp\u00e9rance de vie moyenne d\u2019un patient ?<\/strong><\/p>\n<p>C\u2019est une maladie \u00e0 \u00e9volution rapide dont l\u2019issue est <strong>presque toujours mortelle<\/strong>. En effet, dans 50% des cas, le patient atteint par la maladie de Charcot meurt dans les trois ans apr\u00e8s l\u2019apparition de la maladie. Il existe cependant des cas de survie prolong\u00e9e, mais tr\u00e8s rares.<\/p>\n<\/div><div class=\"fusion-clearfix\"><\/div><\/div><\/div><\/div><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-4 nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-3 fusion_builder_column_1_1 1_1 fusion-one-full fusion-column-first fusion-column-last\" style=\"--awb-bg-size:cover;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-column-wrapper-legacy\"><div class=\"fusion-text fusion-text-3\"><p><a href=\"https:\/\/www.hellocare.com\/\" target=\"_blank\" rel=\"noopener noreferrer\">&gt; Vous avez besoin de parler \u00e0 un dermatologue ?<\/a><\/p>\n<\/div><div class=\"fusion-clearfix\"><\/div><\/div><\/div><\/div><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-5 nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-4 fusion_builder_column_1_1 1_1 fusion-one-full fusion-column-first fusion-column-last\" style=\"--awb-bg-size:cover;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-column-wrapper-legacy\"><div class=\"fusion-title title fusion-title-2 fusion-sep-none fusion-title-text fusion-title-size-three\"><h3 class=\"fusion-title-heading title-heading-left fusion-responsive-typography-calculated\" style=\"margin:0;--fontSize:40;line-height:1.3;\"><h3>SLA : des causes myst\u00e9rieuses<\/h3><\/h3><\/div><div class=\"fusion-text fusion-text-4\"><p>Il existe deux types de SLA : g\u00e9n\u00e9tique (dans 5 \u00e0 10% des cas) et sporadique (90 \u00e0 95% des cas). Sporadique signifie qu\u2019en r\u00e9alit\u00e9, les causes de la maladie de Charcot restent, encore aujourd\u2019hui, tr\u00e8s myst\u00e9rieuses. Cependant, les scientifiques explorent de nombreuses pistes :<\/p>\n<ul>\n<li>L\u2019exposition aux pesticides car les agriculteurs et les footballeurs sont plus touch\u00e9s que le reste de la population<\/li>\n<li>Les traumatismes physiques importants et r\u00e9p\u00e9t\u00e9s<\/li>\n<li>Le sport de haut niveau<\/li>\n<li><a href=\"https:\/\/www.hellocare.com\/blog\/pour-arreter-de-fumer\/\" target=\"_blank\" rel=\"noopener noreferrer\">Le tabagisme<\/a> (actif ou passif)<\/li>\n<li>Certaines bact\u00e9ries ou virus, comme par exemple l\u2019<strong>ent\u00e9rovirus<\/strong><\/li>\n<\/ul>\n<p>Toutefois, ces \u00e9tudes ont \u00e9t\u00e9 men\u00e9es sur une tr\u00e8s petit nombre de patients atteints de SLA et tiennent donc encore largement de l\u2019hypoth\u00e8se.<\/p>\n<\/div><div class=\"fusion-clearfix\"><\/div><\/div><\/div><\/div><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-6 nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-5 fusion_builder_column_1_1 1_1 fusion-one-full fusion-column-first fusion-column-last\" style=\"--awb-bg-size:cover;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-column-wrapper-legacy\"><div class=\"fusion-title title fusion-title-3 fusion-sep-none fusion-title-text fusion-title-size-three\"><h3 class=\"fusion-title-heading title-heading-left fusion-responsive-typography-calculated\" style=\"margin:0;--fontSize:40;line-height:1.3;\"><h3>Diagnostiquer les premiers sympt\u00f4mes de la maladie de Charcot<\/h3><\/h3><\/div><div class=\"fusion-text fusion-text-5\"><p>De m\u00eame que pour de nombreuses maladies neurod\u00e9g\u00e9n\u00e9ratives, les <strong>premiers sympt\u00f4mes de la maladie de Charcot<\/strong> sont souvent difficiles \u00e0 identifier, car pris s\u00e9par\u00e9ment, ils peuvent sembler banals.<br \/>\nEn effet, il peut s\u2019agir de crampes, de contractions musculaires, de faiblesse d\u2019un membre, de troubles de l\u2019\u00e9locution, de difficult\u00e9s \u00e0 m\u00e2cher et \u00e0 avaler\u2026<\/p>\n<p>Ce sont souvent des acc\u00e8s de faiblesse de plus en plus fr\u00e9quent qui m\u00e8nent les m\u00e9decins \u00e0 diagnostiquer la maladie de Charcot. De fait, il n\u2019existe pas de test sp\u00e9cifique qui am\u00e8ne \u00e0 un diagnostic certain.<\/p>\n<\/div><div class=\"fusion-clearfix\"><\/div><\/div><\/div><\/div><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-7 nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-6 fusion_builder_column_1_1 1_1 fusion-one-full fusion-column-first fusion-column-last\" style=\"--awb-bg-size:cover;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-column-wrapper-legacy\"><div class=\"fusion-title title fusion-title-4 fusion-sep-none fusion-title-text fusion-title-size-three\"><h3 class=\"fusion-title-heading title-heading-left fusion-responsive-typography-calculated\" style=\"margin:0;--fontSize:40;line-height:1.3;\"><h3>Les sympt\u00f4mes \u00e0 long terme<\/h3><\/h3><\/div><div class=\"fusion-text fusion-text-6\"><p>Au fil du temps, la SLA aboutira \u00e0 une paralysie compl\u00e8te du corps, \u00e0 l\u2019exception des muscles oculaires. Lorsque les muscles thoraciques sont atteints, le patient doit \u00eatre mis sous assistance respiratoire jusqu\u2019au moment o\u00f9 il meurt, le plus souvent d\u2019insuffisance respiratoire.<\/p>\n<p>Du fait de ces handicaps, il arrive en outre que les patients atteints de la maladie de Charcot soient atteints de <a href=\"https:\/\/www.hellocare.com\/blog\/mieux-comprendre-la-depression\/\" target=\"_blank\" rel=\"noopener noreferrer\">d\u00e9pression<\/a> qui entra\u00eene une alt\u00e9ration de fonctions cognitives comme par exemple la m\u00e9moire ou la prise de d\u00e9cision.<\/p>\n<\/div><div class=\"fusion-clearfix\"><\/div><\/div><\/div><\/div><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-8 nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-7 fusion_builder_column_1_1 1_1 fusion-one-full fusion-column-first fusion-column-last\" style=\"--awb-bg-size:cover;\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-column-wrapper-legacy\"><div class=\"fusion-title title fusion-title-5 fusion-sep-none fusion-title-text fusion-title-size-three\"><h3 class=\"fusion-title-heading title-heading-left fusion-responsive-typography-calculated\" style=\"margin:0;--fontSize:40;line-height:1.3;\"><h3>La crise est l\u00e0 : que faire ? Traiter les sympt\u00f4mes<\/h3><\/h3><\/div><div class=\"fusion-text fusion-text-7\"><p>Jusqu\u2019\u00e0 ce jour, il n\u2019existe malheureusement ni <strong>traitement pour soigner la maladie de Charcot<\/strong> ni pr\u00e9vention efficace. En revanche, il existe un m\u00e9dicament qui ralentirait la progression de la maladie : le Riluzole. En outre, une \u00e9tude am\u00e9ricaine a r\u00e9cemment mis en lumi\u00e8re les b\u00e9n\u00e9fices d\u2019un <a href=\"https:\/\/www.hellocare.com\/blog\/cuisine-medecin-regime\/\" target=\"_blank\" rel=\"noopener noreferrer\">r\u00e9gime riche en antioxydants<\/a> pour freiner l\u2019apparition des sympt\u00f4mes.<\/p>\n<p>Il est cependant possible d\u2019<strong>am\u00e9liorer la qualit\u00e9 de vie<\/strong> des patients en soulageant leurs sympt\u00f4mes gr\u00e2ce \u00e0 des soins de kin\u00e9sith\u00e9rapie et d\u2019orthophonie ainsi qu\u2019en leur fournissant des antidouleurs et des soins palliatifs.<\/p>\n<\/div><div class=\"fusion-clearfix\"><\/div><\/div><\/div><\/div><\/div><div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-9 nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-8 fusion_builder_column_1_1 1_1 fusion-one-full fusion-column-first fusion-column-last fusion-column-inner-bg-wrapper\" style=\"--awb-inner-bg-size:cover;\"><span class=\"fusion-column-inner-bg hover-type-none\"><a class=\"fusion-column-anchor\" href=\"https:\/\/www.hellocare.com\/jesuispatient\/\"><span class=\"fusion-column-inner-bg-image\"><\/span><\/a><\/span><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-column-wrapper-legacy\"><div class=\"fusion-image-element in-legacy-container\" style=\"--awb-caption-title-font-family:var(--h2_typography-font-family);--awb-caption-title-font-weight:var(--h2_typography-font-weight);--awb-caption-title-font-style:var(--h2_typography-font-style);--awb-caption-title-size:var(--h2_typography-font-size);--awb-caption-title-transform:var(--h2_typography-text-transform);--awb-caption-title-line-height:var(--h2_typography-line-height);--awb-caption-title-letter-spacing:var(--h2_typography-letter-spacing);\"><span class=\" fusion-imageframe imageframe-none imageframe-2 hover-type-none\"><a class=\"fusion-no-lightbox\" href=\"https:\/\/www.hellocare.com\/\" target=\"_blank\" aria-label=\"consultation-medecin-en-ligne-hellocare\" rel=\"noopener noreferrer\"><img decoding=\"async\" width=\"768\" height=\"334\" alt=\"consulter un medecin en ligne hellocare\" src=\"data:image\/svg+xml,%3Csvg%20xmlns%3D%27http%3A%2F%2Fwww.w3.org%2F2000%2Fsvg%27%20width%3D%27768%27%20height%3D%27334%27%20viewBox%3D%270%200%20768%20334%27%3E%3Crect%20width%3D%27768%27%20height%3D%27334%27%20fill-opacity%3D%220%22%2F%3E%3C%2Fsvg%3E\" data-orig-src=\"https:\/\/www.hellocare.com\/blog\/wp-content\/uploads\/2019\/06\/consultation-medecin-en-ligne-hellocare-1.jpg\" class=\"lazyload img-responsive wp-image-23483\"\/><\/a><\/span><\/div><div class=\"fusion-clearfix\"><\/div><\/div><\/div><\/div><\/div><\/p>\n","protected":false},"excerpt":{"rendered":"<p>a maladie de Charcot \u2013 aussi appel\u00e9e scl\u00e9rose lat\u00e9rale amyotrophique, SLA ou maladie de Lou Gehrig \u2013 est<\/p>\n","protected":false},"author":28,"featured_media":25684,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"inline_featured_image":false,"footnotes":""},"categories":[575],"tags":[],"class_list":["post-25674","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-sante-generale-medecine"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v26.5 (Yoast SEO v27.6) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>Maladie de Charcot : sympt\u00f4mes, causes et traitement<\/title>\n<meta name=\"description\" content=\"D\u00e9couvrez les symptomes, causes et traitements de la maladie de charlot. 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